Palmitoyl_thioesterase

Palmitoyl thioesterase

palmitoyl-protein thioesterase 1 (ceroid-lipofuscinosis, neuronal 1, infantile)

Identifiers

Symbol PPT1

Alt. Symbols PPT

Entrez 5538

HUGO 9325

OMIM 600722

RefSeq NM_000310

UniProt P50897

Other data

Locus Chr. 1 p32

palmitoyl-protein thioesterase 2

Identifiers

Symbol PPT2

Entrez 9374

HUGO 9326

OMIM 603298

RefSeq NM_138717

UniProt Q9UMR5

Other data

Locus Chr. 6 p21.3

Palmitoyl thioesterase is an enzyme of lipid metabolism which is associated with neuronal ceroid lipofuscinosis.

External links

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v • d • e Hydrolase: esterases (EC 3.1)

3.1.1: Carboxylic ester hydrolases	Cholinesterase (Acetylcholinesterase, Butyrylcholinesterase) - Pectinesterase - 6-phosphogluconolactonase - PAF acetylhydrolase Lipase (Gastric/Lingual, Pancreatic, Lysosomal, Hormone-sensitive, Endothelial, Hepatic, Lipoprotein, Monoacylglycerol, Diacylglycerol) Phospholipase (A1, A2, B)

3.1.2: Thioesterase	Palmitoyl thioesterase - Ubiquitin carboxy-terminal hydrolase L1

3.1.3: Phosphatase	Alkaline phosphatase - Acid phosphatase (Prostatic)/Tartrate resistant acid phosphatase/Purple acid phosphatases - Nucleotidase - Glucose 6-phosphatase - Fructose 1,6-bisphosphatase - Calcineurin - Phosphoprotein phosphatase (PP2A) - OCRL - Pyruvate dehydrogenase phosphatase - Fructose 2,6-bisphosphatase - Protein tyrosine phosphatase - PTEN

3.1.4: Phosphodiesterase	Autotaxin - Phospholipase (C, D) - Sphingomyelin phosphodiesterase - PDE1 - PDE2 - PDE3 - PDE5

3.1.6: Sulfatase	Arylsulfatase B - Steroid sulfatase - Galactosamine-6 sulfatase - Arylsulfatase A - Iduronate-2-sulfatase - N-acetylglucosamine-6-sulfatase

other	Nuclease

v • d • e Metabolism: lipid metabolism - triglyceride and fatty acid enzymes

Lipid production	ATP citrate lyase - Acetyl-CoA carboxylase Fatty acid synthesis/Fatty acid synthase: Beta-ketoacyl-ACP synthase - Β-Ketoacyl ACP reductase - 3-Hydroxyacyl ACP dehydrase - Enoyl ACP reductase triacyl glycerol: Glycerol-3-phosphate dehydrogenase - Thiokinase

Lipid degradation	Acyl transport: Carnitine palmitoyltransferase I - Carnitine-acylcarnitine translocase - Carnitine palmitoyltransferase II Beta oxidation/Mitochondrial trifunctional protein: Acyl CoA dehydrogenase (ACADL, ACADM, ACADS, ACADVL) - Enoyl-CoA hydratase - 3-Hydroxyacyl CoA dehydrogenase - Acetyl-CoA C-acyltransferase to acetyl-CoA: Malonyl-CoA decarboxylase unsaturated (Enoyl CoA isomerase, 2,4 Dienoyl-CoA reductase) odd chain (Propionyl-CoA carboxylase) aldehydes (Long-chain-aldehyde dehydrogenase)

see also disorders